Primary osseous rosai-dorfman disease without lymphadenopathy: A case report on rare entity

Vol 32| Issue 1 | Jan – June 2019 | page: 34-37 | Sukesh A N, Lazar J Chandy, Dennis P Jose, Pushpa Mahadevan

Authors: Sukesh A N [1], Lazar J Chandy [1], Dennis P Jose [1], Pushpa Mahadevan [2]

[1] Department of Orthopaedics, VPS Lakeshore Hospital, Kochi, Kerala, India.
[2] Department of Pathology, VPS Lakeshore Hospital, Kochi, Kerala, India.

Address of Correspondence

Dr. Sukesh A N,
Department of Orthopaedics, VPS Lakeshore Hospital, Kochi, Kerala, India


Introduction: Primary osseous Rosai-Dorfman Disease (RDD) is an unusual manifestation of a rare non- malignant histiocytic proliferative disease. A disease primarily of lymph node sinus with 40% extra nodal involvement . Extra nodal manifestations can occur without lymphadenopathy (28%). Isolated skeletal involvement is very rare, occurring only in 2-8% of all the patients reported to date .

Keywords: Emperipolesis, Lymphadenopathy, Rosai-Dorfman Disease.


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How to Cite this Article: Sukesh A N, Chandy L J, Jose D P, Mahadevan P. Primary osseous Rosai-Dorfman disease without lymphadenopathy: A case report on rare entity. Kerala Journal of Orthopaedics Jan-June 2019; 32(1): 34-37 .

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